Unusual disease in pediatrics: Rosai Dorfman disease
DOI:
https://doi.org/10.51481/amc.v60i1.991Keywords:
Rosai-Dorfman, Sinus histiocytosis, lymph nodesAbstract
Rosai Dorfman's disease is a rare entity characterized by non-painful lymphadenopathies predominantly cervical and submandibular. In the past it had been considered a malignant reticuloendotheliosis, until it was described as a clinical-pathological entity, isolated in 1969 by Rosai and Dorfman. We present the case of a 4-year-old girl, known to be healthy, with an acute condition of febrile sensation, cervical mass and leukocytosis. Laboratory studies did not identify malignancy or infection as an etiology. She was treated with antibiotics without resolution of his adenopathy, which led decided to give conservative management since it had a complete resection.
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- 2018-01-04 (2)
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