Rapunzel syndrome
DOI:
https://doi.org/10.51481/amc.v49i1.295Keywords:
Rapunzel syndrome, trichobezoar, trichophagiaAbstract
We report herein the case of a 12 year- old girl who had a history of learning diffi culties and trichophagia, hepatosplenomegaly and iron defi ciency anemia, Surgical handling was required fi nding a huge trichobezoar extending into the duodenum. A trichobezoar extending towards the small intestine, is called Rapunzel syndrome. Its symptoms are not specifi c and in general its course is benign. Gastric bezoars can occur in the normal stomach due to the ingestion of objects that can not cross the pylorus. Most of the bezoarshappen as complication of gastric surgery because of an altered pyloric function, hypoperistalsis and low concentrations of gastric acid.
Tricobezoars usually present in young women due to voluntary and compulsive intake of hair (trichophagia) that often is the refl ection of a personality disorder.
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References
Duran F, López B, Martínez V, Alamo M, Jacobo D. Rapunzel Syndrome. Rev. Esp Enferm Dig. 2005; 97: 921-2.
West W, Duncan N. CT appearances of the Ranpuzel syndrome: an unusual form of bezoar and gastrointestinal obstruction. Pediatr
Radiol 1998; 28: 315-6
Aguilar A, Rodríguez G, Hernández M. Sindrome de Rapunzel: reporte de un caso. Act Méd Costarric. 2003; 45: 80-83.
Martín A. Hair apparent: Rapunzel syndrome 2005 AMJ Psychiatric 162: 242-248.
Curioso W, Rivera J, Curioso WI. Síndrome de Rapunzel: Reporte de un caso y revisión de literatura. Rev Gastroenterológica Perú. 2002; 22: 168-172.
El Hajjam M, Lakhlouifi A, Bouzidi A, Kadari R. CT features of of a voluminous gastric trichobezoar. Eur J Pediatr Surg. 2001; 11: 131-2.
Ripolles T, García A, Martínez MJ, Gil P. Gastrointestinal bezoars:
sonographic and CT characteristics. Am J Roentgenol 2001;177: 65-9.
Dalshaug GB, Wainer S, Hollar GL. The Rapunzel syndrome causing atypical intussusption in a child: a cause report. J Pediatric Surgery. 1999 34: 479-80.
Klipfel A, Kessle E, Schein M. Rapunzel syndrome causing gastric emphysema and small bowell obstruccion. Surgery. 2003; 133: 120-1
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